ICD-10 Chapter III: Diseases of the blood and blood-forming organs, and certain disorders involving the immune mechanism

see now ICD-10 Chapter II: Neoplasms

D50-D89 - Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

(D50-D53) Nutritional anemias

• () Iron deficiency anaemia
  • () Iron deficiency anaemia secondary to blood loss (chronic)
  • () Sideropenic dysphagia
    • Kelly-Paterson syndrome
    • Plummer-Vinson syndrome
  • () Other iron deficiency anaemias
  • () Iron deficiency anaemia, unspecified

• () Vitamin B12 deficiency anaemia
  • () Vitamin B12 deficiency anaemia due to intrinsic factor deficiency
    • Pernicious anemia
  • () Vitamin B 12 deficiency anaemia due to selective vitamin B 12 malabsorption with proteinuria
    • Megaloblastic hereditary anaemia
  • () Transcobalamin II deficiency
  • () Other dietary vitamin B 12 deficiency anaemia
  • () Other vitamin B 12 deficiency anaemias
  • () Vitamin B 12 deficiency anaemia, unspecified

• () Folate deficiency anaemia
  • () Dietary folate deficiency anaemia
    • Nutritional megaloblastic anaemia
  • () [...]-induced folate deficiency anaemia
  • () Other folate deficiency anaemias
  • () Folate deficiency anaemia, unspecified

• () Other nutritional anaemias
  • () Protein deficiency anaemia
  • () Other megaloblastic anaemias, not elsewhere classified
  • () Scorbutic anaemia
  • () Other specified nutritional anaemias
  • () Nutritional anaemia, unspecified

(D55-D59) Haemolytic anaemias

• () Anaemia due to enzyme disorders
  • () Anaemia due to glucose-6-phosphate dehydrogenase (G6PD) deficiency
    • Favism
    • G6PD deficiency anaemia
  • () Anaemia due to other disorders of glutathione metabolism
  • () Anaemia due to disorders of glycolytic enzymes
    • hexokinase deficiency
    • pyruvate kinase deficiency
    • triose-phosphate isomerase deficiency
  • () Anaemia due to disorders of nucleotide metabolism
  • () Other anaemias due to enzyme disorders
  • () Anaemia due to enzyme disorder, unspecified

• () Thalassaemia
  • () Alpha thalassaemia
  • () Beta thalassaemia
  • () Delta-beta thalassaemia
  • () Thalassaemia trait
  • () Hereditary persistence of fetal haemoglobin (HPFH)
  • () Other thalassaemias
  • () Thalassaemia, unspecified

• () Sickle-cell disorders
  • () Sickle-cell anaemia with crisis
  • () Sickle-cell anaemia without crisis
  • () Double heterozygous sickling disorders
  • () Sickle-cell trait
  • () Other sickle-cell disorders

• () Other hereditary haemolytic anaemias
  • () Hereditary spherocytosis
    • Acholuric (familial) jaundice
    • Congenital (spherocytic) haemolytic icterus
    • Minkowski-Chauffard syndrome
  • () Hereditary elliptocytosis
    • Elliptocytosis (congenital)
    • Ovalocytosis (congenital)(hereditary)
  • () Other haemoglobinopathies
    • Abnormal haemoglobin NOS
    • Congenital Heinz body anaemia
    • Haemoglobinopathy NOS
    • Unstable haemoglobin haemolytic disease
  • () Other specified hereditary haemolytic anaemias
    • Stomatocytosis

• () Acquired haemolytic anaemia
  • () [...]-induced autoimmune haemolytic anaemia
  • () Other autoimmune haemolytic anaemias
    • Warm autoimmune hemolytic anemia
  • () [...]-induce nonautoimmune haemolytic anaemia
  • () Haemolytic-uraemic syndrome
  • () Other nonautoimmune haemolytic anaemias
    • Microangiopathic hemolytic anemia
  • () Paroxysmal nocturnal haemoglobinuria (Marchiafava-Micheli)
  • () Haemoglobinuria due to haemolysis from other external causes
    • paroxysmal cold haemoglobinuria
  • () Other acquired haemolytic anaemias
  • () Acquired haemolytic anaemia, unspecified

(D60-D64) Aplastic and other anaemias

• () Acquired pure red cell aplasia (erythroblastopenia)

• () Other aplastic anaemias
  • () Constitutional aplastic anaemia
    • Blackfan-Diamond syndrome
    • Familial hypoplastic anaemia
    • Fanconi's anaemia
    • Pancytopenia with malformations
  • () [...]-induced aplastic anaemia
  • () Aplastic anaemia due to other external agents
  • () Idiopathic aplastic anaemia
  • () Other specified aplastic anaemias
  • () Aplastic anaemia, unspecified
    • Hypoplastic anaemia NOS
    • Medullary hypoplasia
    • Panmyelophthisis

• () Acute posthaemorrhagic anaemia
• () Anaemia in chronic diseases classified elsewhere

• () Other anaemias
  • () Hereditary sideroblastic anaemia
  • () Secondary sideroblastic anaemia due to disease
  • () Secondary sideroblastic anaemia due to drugs and toxins
  • () Other sideroblastic anaemias
  • () Congenital dyserythropoietic anaemia
  • () Other specified anaemias
  • () Anaemia, unspecified

(D65-D69) Coagulation defects, purpura and other haemorrhagic conditions

• () Disseminated intravascular coagulation (defibrination syndrome)
  • Afibrinogenaemia, acquired
  • Consumption coagulopathy
  • Diffuse or disseminated intravascular coagulation (DIC)
  • Fibrinolytic haemorrhage, acquired
  • Fibrinolytic purpura
  • Purpura fulminans

• () Hereditary factor VIII deficiency
  • Haemophilia A

• () Hereditary factor IX deficiency
  • Christmas disease
  • Haemophilia B

• () Other coagulation defects
  • () Von Willebrand's disease
  • () Hereditary factor XI deficiency
    • Haemophilia C
  • () Hereditary deficiency of other clotting factors
  • () Haemorrhagic disorder due to circulating anticoagulants
  • () Acquired coagulation factor deficiency
  • () Other specified coagulation defects
  • () Coagulation defect, unspecified

• () Purpura and other haemorrhagic conditions
  • () Allergic purpura
    • anaphylactoid purpura
    • Henoch-Schönlein purpura
  • () Qualitative platelet defects
    • Bernard-Soulier syndrome (giant platelet)
    • Glanzmann's disease
    • Grey platelet syndrome
    • Thromboasthenia (haemorrhagic)(hereditary)
    • Thrombocytopathy
  • () Other nonthrombocytopenic purpura
  • () Idiopathic thrombocytopenic purpura
    • Evans' syndrome
  • () Other primary thrombocytopenia
  • () Secondary thrombocytopenia
  • () Thrombocytopenia, unspecified
  • () Other specified haemorrhagic conditions
  • () Haemorrhagic condition, unspecified

(D70-D77) Other diseases of blood and blood-forming organs

• () Agranulocytosis
  • Agranulocytic angina
  • Infantile genetic agranulocytosis
  • Kostmann's disease
  • Neutropenia, NOS

• () Functional disorders of polymorphonuclear neutrophils
  • Cell membrane receptor complex (CR3) defect
  • Chronic (childhood) granulomatous disease
  • Congenital dysphagocytosis
  • Progressive septic granulomatosis

• () Other disorders of white blood cells
  • () Genetic anomalies of leukocytes
    • Alder anomaly
    • May-Hegglin anomaly
    • Pelger-Huët anomaly
  • () Eosinophilia
  • () Other specified disorders of white blood cells
    • Leukaemoid reaction: lymphocytic, monocytic, myelocytic
    • Leukocytosis
    • Lymphocytosis (symptomatic)
    • Lymphopenia
    • Monocytosis (symptomatic)
    • Plasmacytosis
  • () Disorder of white blood cells, unspecified

• () Diseases of spleen
  • () Hyposplenism
  • () Hypersplenism
  • () Chronic congestive splenomegaly
  • () Abscess of spleen
  • () Cyst of spleen
  • () Infarction of spleen
  • () Other diseases of spleen
  • () Disease of spleen, unspecified

• () Methaemoglobinaemia
  • () Congenital methaemoglobinaemia
    • Congenital NADH-methaemoglobin reductase deficiency
    • Haemoglobin-M (Hb-M) disease
    • Methaemoglobinaemia, hereditary
  • () Other methaemoglobinaemias
    • Acquired methaemoglobinaemia (with sulfhaemoglobinaemia)
    • Toxic methaemoglobinaemia
  • () Methaemoglobinaemia, unspecified

• () Other diseases of blood and blood-forming organs
  • () Familial erythrocytosis
  • () Secondary polycythaemia
  • () Essential thrombocytosis
  • () Other specified diseases of blood and blood-forming organs
    • Basophilia
  • () Disease of blood and blood-forming organs, unspecified

• () Certain diseases involving lymphoreticular tissue and reticulohistiocytic system
  • () Langerhans' cell histiocytosis, not elsewhere classified
    • Eosinophilic granuloma
    • Hand-Schüller-Christian disease
    • Histiocytosis X (chronic)
  • () Haemophagocytic lymphohistiocytosis
    • Familial haemophagocytic reticulosis
  • () Haemophagocytic syndrome, infection-associated
  • () Other histiocytosis syndromes
    • Reticulohistiocytoma (giant-cell)
    • Sinus histiocytosis with massive lymphadenopathy
    • Xanthogranuloma

• () Other disorders of blood and blood-forming organs in diseases classified elsewhere

(D80-D89) Certain disorders involving the immune mechanism

• () Immunodeficiency with predominantly antibody defects
  • () Hereditary hypogammaglobulinaemia
    • Autosomal recessive agammaglobulinaemia (Swiss type)
    • X-linked agammaglobulinaemia (Bruton) (with growth hormone deficiency)
  • () Nonfamilial hypogammaglobulinaemia
    • Agammaglobulinaemia with immunoglobulin-bearing B-lymphocytes
    • Common variable agammaglobulinaemia (CVAgamma)
    • Hypogammaglobulinaemia NOS
  • () Selective deficiency of immunoglobulin A (IgA)
  • () Selective deficiency of immunoglobulin G (IgG) subclasses
  • () Selective deficiency of immunoglobulin M (IgM)
  • () Immunodeficiency with increased immunoglobulin M (IgM)
  • () Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia
  • () Transient hypogammaglobulinaemia of infancy
  • () Other immunodeficiencies with predominantly antibody defects
    • Kappa light chain deficiency
  • () Immunodeficiency with predominantly antibody defects, unspecified

• () Combined immunodeficiencies
  • () Severe combined immunodeficiency (SCID) with reticular dysgenesis
  • () Severe combined immunodeficiency (SCID) with low T-cell and B-cell numbers
  • () Severe combined immunodeficiency (SCID) with low or normal B-cell numbers
  • () Adenosine deaminase deficiency (ADA)
  • () Nezelof's syndrome
  • () Purine nucleoside phosphorylase deficiency (PNP)
  • () Major histocompatibility complex class I deficiency
    • Bare lymphocyte syndrome
  • () Major histocompatibility complex class II deficiency
  • () Other combined immunodeficiencies
    • Biotin-dependent carboxylase deficiency
  • () Combined immunodeficiency, unspecified
    • Severe combined immunodeficiency disorder (SCID) NOS

• () Immunodeficiency associated with other major defects
  • () Wiskott-Aldrich syndrome
    • Immunodeficiency with thrombocytopenia and eczema
  • () Di George's syndrome
  • () Immunodeficiency with short-limbed stature
  • () Immunodeficiency following hereditary defective response to Epstein-Barr virus
    • X-linked lymphoproliferative disease
  • () Hyperimmunoglobulin E syndrome (IgE)
• () Common variable immunodeficiency

• () Other immunodeficiencies
  • () Lymphocyte function antigen-1 (LFA-1) defect
  • () Defects in the complement system
    • C1 esterase inhibitor deficiency (C1-INH)
  • () Other specified immunodeficiencies
  • () Immunodeficiency, unspecified

• () Sarcoidosis
  • () Sarcoidosis of lung
  • () Sarcoidosis of lymph nodes
  • () Sarcoidosis of lung with sarcoidosis of lymph nodes
  • () Sarcoidosis of skin
  • () Sarcoidosis of other and combined sites
• () Other disorders involving the immune mechanism, not elsewhere classified
  • () Polyclonal hypergammaglobulinaemia
    • Benign hypergammaglobulinaemic purpura
    • Polyclonal gammopathy NOS
  • () Cryoglobulinaemia
  • () Hypergammaglobulinaemia, unspecified
  • () Other specified disorders involving the immune mechanism, not elsewhere classified
  • () Disorder involving the immune mechanism, unspecified

See also

• List of ICD-10 codes
• International Statistical Classification of Diseases and Related Health Problems
• List of ICD-9 codes 140-239: Neoplasms

fr:CIM-10 Chapitre 03 : Maladies du sang et des organes hématopoïétiques et certains troubles du système immunitaire hr:MKB-10 D50-D89 hu:BNO-10-02 – Daganatok no:ICD-10 kapittel III: D50-D89 - Sykdommer i blod og bloddannende organer og visse tilstander som angår immunsystemet pt:CID-10 Capítulo II: Neoplasias (tumores); Capítulo III: Doenças do sangue e dos órgãos hematopoéticos e alguns transtornos imunitários ru:МКБ-10: Класс II th:ICD-10 บท C และ D: เนื้องอก โรคเลือดและอวัยวะสร้างเลือด และโรคภูมิคุ้มกันผิตปกติ